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Spontaneous coronary artery dissection as a marker of undifferentiated connective tissue dysplasia: a case report

https://doi.org/10.15829/1728-8800-2021-2973

Abstract

The article presents a case report of spontaneous coronary artery dissection (SCAD) in the young woman with signs of undifferentiated connective tissue dysplasia (UCTD). The patient was admitted urgently with a clinical and electrocardiographic signs of acute ST-segment elevation coronary syndrome. The patient underwent a coronary angiography, which revealed a type D linear intimal dissection. The decision was made to perform balloon vasodilation with the placement of a drug-eluting stent. With multicomponent therapy, the patient’s condition improved. Physical examination revealed external markers of UCTD. Therefore, it was quantified by systems and organs. The patient had no other cardiovascular diseases, previous infection, or other trigger factors. She was discharged with recommendations to continue the prescribed therapy. This case report demonstrates SCAD as a rare cause of acute myocardial infarction in a young patient. The background for SCAD development in this case was UCTD. Algorithms for managing patients with SCAD against the background of UCTD have not been defined and require further study.

About the Authors

Ya. B. Khovaeva
E.A. Wagner Perm State Medical University
Russian Federation

Perm



A. L. Korovin
S.N. Grinberg City Clinical Hospital
Russian Federation

Perm



Ya. A. Sychugov
S.N. Grinberg City Clinical Hospital
Russian Federation

Perm



L. V. Ermachkova
E.A. Wagner Perm State Medical University
Russian Federation

Perm



N. P. Moiseenko
E.A. Wagner Perm State Medical University
Russian Federation

Perm



References

1. Saw J, Mancini G, Humphries K. Contemporary Review on Spontaneous Coronary Artery Dissection. J Am Coll Cardiol. 2016;68(3):297-312. doi:10.1016/j.jacc.2016.05.034.

2. Zhukova NS, Shahnovich RM, Merkulova IN, et al. Spontaneous coronary artery dissection. Kardiologiia. 2019;59(9):52-63. (In Russ.) doi:10.18087/cardio.2019.9.10269.

3. Vatutin NT, Taradin GG, Bort DV, et al. Spontaneous coronary artery dissection case (review and case presentation). Arhiv vnutrennej mediciny. 2019;9(1):23-30. (In Russ.) doi:10.20514/2226-6704-2019-9-1-23-30.

4. Akatova EV, Boginskaja OA, Vershinina MV, et al. Connective tissue dysplasia in primary care. M.: KST Interforum, 2016. 520 p. (In Russ.) ISBN: 978-5-9908980-0-4.

5. Connective tissue dysplasia: clinical guidelines 2017. Russian Scientific Medical Society of Physicians (RSMSP). 181 p. (In Russ.) https://www.rnmot.ru/public/uploads/2018/RNMOT/Клинические%20рекомендации_ДСТ%20сайт%2016.02.18г_.pdf. (13 апреля 2021).

6. Henkin S, Negrotto SM, Tweet MS, et al. Spontaneous coronary artery dissection and its association with heritable connective tissue disorders. Heart. 2016;102:876-81. doi:10.1136/heartjnl-2015-308645.

7. Grond-Ginsbach C, Engelter ST. Genetics of Spontaneous Coronary Artery Dissection Gains New Momentum. Circ Genom Precis Med. 2018;11:e002148. doi:10.1161/CIRCGEN.118.002148.

8. Perekal’skaja MA, Volkova II, Ostanina JuO, et al. Vascular pathology in inherited connective tissue disorders. Russian Journal of Cardiology. 2013;(2):83-8. (In Russ.) doi:10.15829/1560-4071-2013-2-83-88


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For citations:


Khovaeva Ya.B., Korovin A.L., Sychugov Ya.A., Ermachkova L.V., Moiseenko N.P. Spontaneous coronary artery dissection as a marker of undifferentiated connective tissue dysplasia: a case report. Cardiovascular Therapy and Prevention. 2021;20(7):2973. (In Russ.) https://doi.org/10.15829/1728-8800-2021-2973

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ISSN 1728-8800 (Print)
ISSN 2619-0125 (Online)